NUTRITIONAL INFORMATION

Because there is no current standard of care for Duarte galactosemia (DG), it is up to families and
their healthcare providers to discuss and decide which approach is best for them.  There is a broad
range of options.  Examples include:









Regardless of diet, some healthcare providers might recommend doing follow-up lab tests to check
the baby’s galactose metabolite levels in blood or urine. If the baby has been eating a diet that
restricts galactose, and the family wants to consider relaxing the restriction, the baby’s healthcare
provider might recommend doing a “galactose challenge” sometime around the baby’s first birthday.
To read more about a galactose challenge, see the For Healthcare Professionals page.

What is galactose and where does it come from?
Galactose is a natural sugar that is found at high levels in some foods, like milk, and at lower or very
low levels in other foods. Galactose is also made at low levels by the human body.

Foods high in galactose:
Galactose is present at very high levels in milk. This includes human breast milk, cow’s milk, and
other natural forms of milk. The galactose in milk comes from lactose, or milk sugar, which is broken
down by normal digestion to give glucose and galactose. Galactose is also found at high levels in
most dairy products, including soft cheeses, ice cream, yogurt, etc. Galactose is not present at high
levels in milk substitutes such as soy formula or soy milk, almond milk, or rice milk.

For more detailed nutritional information about high and low galactose-containing foods and their
alternatives, please visit Galactosemia Foundation Diet Resources.
Full dietary restriction of milk, milk formula, and dairy products for the first 12 months of life, or
Partial dietary restriction of milk, such as alternated feedings between breast milk and low
galactose formula, or some other combination of milk formula and low galactose feedings, or
No diet restriction.
Of note, some families might choose to restrict milk and high galactose foods for more than 12
months, or might choose to follow other diet protocols.